Author
Information
Sarita
Channawar*, Devendra Patil**, Anuya Pawde***, A. R. Chauhan***
(*
Assistant Professor, ** Third tear Resident, *** Senior Registrar,
**** Additional Professor. Department of Obstetrics and Gynecology,
Seth G.S. Medical College and K.E.M Hospital, Mumbai, India.)
Abstract
Ovarian stromal
hyperplasia (OSH) and hyperthecosis (OHT) are rare causes of
virilization in postmenopausal women. A 60 year old postmenopausal
woman with virilization due to bilateral ovarian stromal hyperplasia
is discussed here.
Introduction
Hirsutism
in women may be defined as excess thick (terminal) hair growth in
body parts where normally there is no presence of terminal hair. It
is an early sign of hyperandrogenism. The causes of hirsuitism in
postmenopausal women can be many, like ovarian stromal hyperplasia,
ovarian hyperthecosis, ovarian tumors, adrenal tumors, Cushing’s
syndrome and insulin resistance syndrome. Ovarian stromal hyperplasia
and hyperthecosis are very rare causes of hyperandrogenism. The serum
testosterone levels show moderate elevation resulting into
virilisation. This case report highlights ovarian stromal hyperplasia
as a cause hyperandrogenism and virilization in a postmenopausal
woman.
Case
Report
A
60 year old parous woman, postmenopausal since ten years, presented
with a history of worsening hirsutism (increasing facial hair) since
1-2 months, and excessive weight gain since 1 year (BMI of 34.57).
She was a known case of diabetes mellitus and hypertension on
treatment since 10 years and 2 years respectively, and had undergone
cholecystectomy 10 years ago. On general examination, she had facial
mooning and excessive facial hair. Abdominal examination revealed
central obesity but no palpable lump. Local genital examination
showed mild clitoromegaly; per speculum examination showed healthy
cervix and vagina; on bimanual examination the uterus was normal in
size with no palpable adnexal mass.
Figure:
1 Hirsuitism
Figure:
2 Clitoromegaly
The patient was
managed jointly with an endocrinologist. Her investigations were
directed at finding the source of androgen excess and ruling out
Cushing’s syndrome. The serum concentration of testosterone (25.88
ng/ml) and dehydroepiandrosterone sulphate (DHEAS - 54.22 ug/ml)
were significantly elevated, while level of 17-hydroxy-progesterone
(15.68 ng/ dl), aldosterone ( 29.13 ng/dl), androstenedione (26.03
ng/dl), deoxycortisol (33.85 ng/ml), cortisol (12.9 ug/ml),
corticosterone (159.74 ng/ml), FSH 45 mIU/ml, LH 13.78 mIU/ml
(postmenopausal) were normal. Pelvic ultrasonography showed normal
uterus with bulky ovaries without follicles, vascularity or any solid
cystic lesion. Computerized tomography (CT) of the abdomen and pelvis
was suggestive of bilateral adrenal hyperplasia, with small cortical
cyst in left kidney and bilateral ovaries bulky for age.
The
extent of adrenal hyperplasia was considered normal for her
postmenopausal age. The basal level of serum cortisol (22.31), oral
dexamethasone suppression cortisol (0.97) and basal ACTH (33.7) were
normal. So adrenal cause of hyperandrogenism was ruled out and
provisional diagnosis of ovarian nonmalignant cause of peripheral
androgen excess was made. The plan of management was surgery with
bilateral oophorectomy for removal of the source of excess androgen;
accordingly she underwent total abdominal hysterectomy with bilateral
salpingo-oophorectomy. Intraoperatively, the uterus was smaller than
normal size, but both ovaries were bulky and smooth. Her
postoperative course was uneventful and she was discharged on
postoperative day 5, at which time her repeat serum testosterone
level was 0.9 ng/ml, within normal range. The histopathology report
was suggestive of bilateral ovarian stromal hyperplasia with no
evidence of malignancy.
Discussion
Ovarian
stromal hyperplasia (OSH) is the nodular or diffuse proliferation of
ovarian stroma, and ovarian hyperthecosis (OHT) is stromal
proliferation with luteinised stromal cells. Both OSH and OHT are
non-neoplastic pathologies involving both ovaries, causing excess
androgen production, and usually seen in postmenopausal females.
OSH and OHT are seen in postmenopausal women but these
histopathological conditions rarely cause elevation in testosterone
and virilisation. A
wide range of clinical manifestations like hirsutism, virilization,
abnormal menses, obesity, hypertension and insulin resistance are
seen.[1]
Mild
diffuse bilateral hyperplasia is found in one third of perimenopausal
and postmenopausal women.
The case presented here is a postmenopausal patient with markedly
elevated testosterone levels and signs of virilization secondary to
ovarian stromal hyperplasia.
The
cause of significantly increased androgen secretion in postmenopausal
patients with OSH and OHT is increased gonadotropin secretion which
causes stimulation of gonadal cells to produce testosterone and
androstenedione. Androgens are aromatized to estrogens by granulosa
cells in premenopausal women, but this does not occur to the same
degree in postmenopausal women, leading to predominance of
androgens.[2]
The
increase in estrogen production may result in increased risk of
endometrial hyperplasia and carcinoma, especially in postmenopausal
women.[3]
It is also necessary
to rule out ovarian and adrenal tumors in postmenopausal woman with
hirsutism and marked hyper-androgenism.
Androgen
levels are important for diagnosis; testosterone and DHEA-S should be
measured first and are usually found high for postmenopausal age.[4]
If serum total testosterone level is >150 ng/ml, imaging of
adrenals and ovaries must be done. A transvaginal pelvic ultrasound
and CT scan or magnetic resonance imaging are very useful for
diagnosis.[5]
If not diagnosed on these modalities, selective ovarian venous
sampling has been described.[6] Once
the diagnosis is made using history, clinical examination, laboratory
parameters and imaging, the patient should undergo bilateral
oophorectomy to remove the cause of excess androgens and to reverse
virilization.[7]
Conclusion
Hyperandrogenism in
postmenopausal women is a diagnostic challenge. The causes of
postmenopausal virilization may be associated with adrenal or ovarian
androgen-secreting tumors or with benign conditions. The development
of virilization can be progressive (characteristic of benign causes),
or rapid (characteristic of malignant tumors), and detailed clinical
history is critical to differentiate these conditions. Imaging
techniques do not always reveal the cause of hyperandrogenism, in
which case adrenal and/or ovarian venous sampling, though difficult,
may be used. The cases of postmenopausal severe and acute onset
virilization, where Cushing’s syndrome is ruled out and adrenal
imaging is normal, should be treated with bilateral oophorectomy.
This approach is necessary to avoid further delay in definitive
treatment.
References
- Rousset P, Gompel A, Christin-Maitre S, Pugeat M, Hugol D, Ghossain MA, Buy JN. Ovarian hyperthecosis on grayscale and colour Doppler ultrasound, Ultrasound Obstet Gynaecol 2008; 32(5):694-9.
- Goldman JM, Kapadia LJ. Postgrad Med J. Virilization in a postmenopausal woman due to ovarian stromal hyperthecosis Postgrad Med J 1991;67(785): 304-306.
- Nagamani M, Hannigan EV, Dinh TV, Stuart CA. Hyperinsulinemia and stromal luteinization of the ovaries in postmenopausal women with endometrial cancer. J Clin Endocrinol Metab 1988;67(1):144-8.
- Martin KA, Chang RJ, Ehrmann DA, Ibanez L, Lobo RA, Rosenfield RL, et al. Evaluation and treatment of hirsuitism in premenopausal women; an endocrine society clinical practise guideline. J Clin Endocrinol Metab 2008;93(4):1105-20.
- Rothman MS, Wierman ME. How should postmenopausal androgen excess be evaluated? Clin Endocrinol 2011;75(2):160-4.
- Levens ED, Whitcomb BW, Csokmay JM, Nieman LK. Selective venous sampling for androgen producing pathology. Clin Endocrinology. 2009;70(4):606-614.
- Alpanes M, Gonzalez-Casbas JM, Sanchez J, Pian H, Escobar-Morreale HF. Management of postmenopausal virilization. J Clin Endocrinol Metab 2012;97(8):2584-8.
Author
Information
Channawar
S, Patil D, Pawde A, Chauhan AR.
Postmenopausal Ovarian Stromal Hyperplasia. JPGO
2014 Volume 1 Issue 9. Available from : http://www.jpgo.org/2014/09/postmenopausal-ovarian-stromal.html